The McCune-Albright syndrome is rare disease diagnosed by the clinical triad, fibrous\ndysplasia, caf�©-au lait skin pigmentations and endocrine hyperfunction. Those\npatients with bone issues could have various surgeries under general anesthesia.\nAirway abnormality and various endocrine abnormalities should be considered during\ngeneral anesthesia for McCune-Albright syndrome patients. A 15-year-old male\nwith McCune-Albright syndrome was admitted with complaint of right nasal obstruction\noriginated from fibrous dysplasia. Endoscopic resection of nasal cavity lesion\nwas scheduled under navigation system guidance. Difficult airway could be anticipated\ndue to protrusion of maxilla and right nostril. Awake fiberoptic intubation\nwas performed by spray-as-you-go technique. When an anesthesiologist expects to\ntake care of the patient with the McCune-Albright syndrome, the most appropriate\nanesthetic induction and tracheal intubation technique should be selected, and multiple\nbackup instruments such as supraglottic device, video laryngoscope and fiberoptic\nbronchoscopy should be prepared.
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